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| CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Basic information |
| Product Name: | CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE | | Synonyms: | EC 2.1.3.3;CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE;ORNITHINE TRANSCARBAMYLASE;ORNITHINE CARBAMYLTRANSFERASE;ornithine carbamoyl transferase from strept. faec.;ornithine carbamyltransferase from*streptococcus;Carbamoyltransferase, ornithine;ORNITHINE CARBAMYLTRANSFERASE FROM*STREP TOCOCCUS FA | | CAS: | 9001-69-8 | | MF: | | MW: | 0 | | EINECS: | 232-625-1 | | Product Categories: | | Mol File: | Mol File |
| CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Chemical Properties |
| storage temp. | −20°C | | form | lyophilized powder |
| CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Usage And Synthesis |
| Description | An enzyme that catalyzes the transfer of a carbamyl
group from carbamyl phosphate to ornithine to form citrulline; it is a constituent reaction of the urea cycle. This enzyme normally
occurs in the mitochondria of liver cells, but only to a minute extent
in serum. Since it does not occur to a significant extent in serum,
kidney, brain, etc., and only 1% or 2% of the hepatic concentration
occurs in small intestine, its presence in serum is a specific indica_x0002_tion of damage to liver cells. | | Biochem/physiol Actions | Mutations in ornithine transcarbamylase cause Ornithine transcarbamylase deficiency which prevents the clearance of the byproduct ammonia leading to hyperammonemia. |
| CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Preparation Products And Raw materials |
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