Ethylmalonic acid -d 3 is the deuterium labeled Ethylmalonic acid ( HY-34740 ). Ethylmalonic acid is a short-chain organic dicarboxylic acid. Ethylmalonic acid synergistically induces mitochondrial permeability transition (MP) with Ca 2+ , inhibits Mi-CK , and disrupts mitochondrial energy metabolism . Ethylmalonic acid can be used in the research of SCADD, EE and other genetic metabolic diseases characterized by EMA accumulation.
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